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Journal of The Korean Society of Emergency Medicine 1995;6(1): 132-136. |
A CASE OF VASOOCCLUSIVE CRISIS DUE TO SICKLE CELL DISEASE
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Taeg Hwan Bae1, Yoon Seok Jung1, Jun Sig Kim1, Hyun Soo Kim2, Hugh Chui Kim2, Yun Sik Kwak3, Joon Pil Cho1 |
1Department of Emergency Medicine, Ajou University School of Medicine, Suwon, Korea 2Department of Hematology-Oncolod, Ajou University School of Medicine, Suwon, Korea 3Department of Clinical Pathology, Ajou University School of Medicine, Suwon, Korea |
Published online: June 30, 1995. |
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ABSTRACT |
The sickle cell disease are a group of hemoglobin disorders characterized by red cells that undergo sickle shape transformation when they are deoxygenated. Sickle cell disease is transmit ted as an autosomal recessive trait. This unusual property, due to the polymerization of sickle hemoglobin results in anemia and vasoocclusive complication.1) The most clinically significant of these disease are sickle cell anemia, sickle cell hemoglobin C disease, and sickle cell beta thalassemia. Symptoms of pallor, fever, abdominal and joint pain, enlargement of the liver and spleen, swelling of hands and feet first appear near the latter part of the first year of life. Intravascular sickling affects all organs. For clinical and therapeutic purposes, exacerbations may be classified as vasoocclusive or pain, aplastic, hemolytic or sequestration crisis. we experienced a 22 year old female patient who suffered severe multiple joint pain and back pain thought to be caused by vaso-occlussive phenomena.
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Key words:
Sickle cell disease, Vasa-occlusive crisis,
Sickle cell disease, Vaso-occlusive crisis
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